Primary biliary cholangitis and Primary sclerosing cholangitis
Primary Biliary Cholangitis(PBC) Feature Primary Sclerosing Cholangitis(PSC) Chronic autoimmune destructionof small intrahepatic bile ducts (IHBD) Definition Chronic inflammation and fibrosis ofintra (IHBD) & extrahepatic bileducts (EHBD) Mostly women GenderPredilection Mostly men 40–60 years Age of Onset 20–40 years – Sjogrens syndrome – Rheumatoid arthritis (RA)– Celiac disease– Systemic sclerosis AssociatedConditions Ulcerative colitis(in ~70% cases) AMA […]
